Moyamoya disease: report of three cases in Brazilian patients

Moyamoya disease: report of three cases in Brazilian patients

Alternative title Doença de Moyamoya: relato de três pacientes brasileiros
Author Franco, Clélia Maria Ribeiro Google Scholar
Fukujima, Marcia Maiumi Autor UNIFESP Google Scholar
Oliveira, Roberto de Magalhães Carneiro de Google Scholar
Gabbai, Alberto Alain Autor UNIFESP Google Scholar
Institution Universidade Federal de São Paulo (UNIFESP)
Abstract Moyamoya disease (MMD) is a chronic occlusive cerebrovascular disease of unknown etiology reported mainly in the Japanese. Most cases occur in children. The disease is rare in non-Oriental adults manifesting itself mostly as intracerebral hemorrhages. We describe MMD in 2 non-Oriental young adults and one adolescent that developed cerebral infarctions. The adults were medicated with aspirin and no medication was given to the adolescent. All patients did not deteriorate in a follow-up period from 1 to 4 years. Although rare, MMD is an important cause of stroke in young individuals and may well be underreported: only 18 patients have been reported till 1997 in Brazil. Neurologists should include MMD in differential diagnosis of ischemic and hemorrhagic strokes in young adults.

A doença de moyamoya (DMM) é patologia cerebrovascular oclusiva crônica de etiologia desconhecida, descrita inicialmente em japoneses. A maioria dos casos ocorre em crianças. Relatamos três casos de DMM, dois adultos e um adolescente não-orientais que apresentaram a forma isquêmica da doença, embora adultos apresentem principalmente a forma hemorrágica. Todos foram submetidos a tratamento conservador e acompanhados durante um a quatro anos, sem piora ou recorrência dos déficits neurológicos. A DMM é uma incomum mas importante causa de acidente vascular cerebral isquêmico, sendo subdiagnosticada em nosso país, onde apenas 18 casos foram descritos até o 1997.
Keywords moyamoya disease
adult
chronic occlusive cerebrovascular disorder
stroke
doença de moyamoya
adulto
doença cerebrovascular
acidente vascular cerebral
Language English
Date 1999-06-01
Published in Arquivos de Neuro-Psiquiatria. Academia Brasileira de Neurologia - ABNEURO, v. 57, n. 2B, p. 371-376, 1999.
ISSN 0004-282X (Sherpa/Romeo)
Publisher Academia Brasileira de Neurologia - ABNEURO
Extent 371-376
Origin http://dx.doi.org/10.1590/S0004-282X1999000300005
Access rights Open access Open Access
Type Article
SciELO ID S0004-282X1999000300005 (statistics in SciELO)
URI http://repositorio.unifesp.br/handle/11600/785

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