Brazilian Guidelines for Hereditary Angioedema Management-2017 Update Part 1: Definition, Classification and Diagnosis

Brazilian Guidelines for Hereditary Angioedema Management-2017 Update Part 1: Definition, Classification and Diagnosis

Author Giavina-Bianchi, Pedro Google Scholar
Arruda, Luisa Karla Google Scholar
Aun, Marcelo V. Google Scholar
Campos, Regis A. Google Scholar
Chong-Neto, Herberto J. Google Scholar
Constantino-Silva, Rosemeire N. Google Scholar
Fernandes, Fatima R. Google Scholar
Ferraro, Maria F. Google Scholar
Ferriani, Mariana P. L. Google Scholar
Franca, Alfeu T. Google Scholar
Fusaro, Gustavo Google Scholar
Garcia, Juliana F. B. Google Scholar
Komninakis, Shirley Google Scholar
Maia, Luana S. M. Google Scholar
Mansour, Eli Google Scholar
Moreno, Adriana S. Google Scholar
Motta, Antonio A. Google Scholar
Pesquero, Joao B. Autor UNIFESP Google Scholar
Portilho, Nathalia Google Scholar
Rosario, Nelson A. Google Scholar
Serpa, Faradiba S. Google Scholar
Sole, Dirceu Google Scholar
Takejima, Priscila Google Scholar
Toledo, Eliana Google Scholar
Valle, Solange O. R. Google Scholar
Veronez, Camila L. Autor UNIFESP Google Scholar
Grumach, Anete S. Google Scholar
Abstract Hereditary angioedema is an autosomal dominant disease characterized by recurrent angioedema attacks with the involvement of multiple organs. The disease is unknown to many health professionals and is therefore underdiagnosed. Patients who are not adequately diagnosed and treated have an estimated mortality rate ranging from 25% to 40% due to asphyxiation by laryngeal angioedema. Intestinal angioedema is another important and incapacitating presentation that may be the main or only manifestation during an attack. In this article, a group of experts from the "Associacao Brasileira de Alergia e Imunologia (ASBAI)'' and the "Grupo de Estudos Brasileiro em Angioedema Hereditario (GEBRAEH)'' has updated the Brazilian guidelines for the diagnosis and treatment of hereditary angioedema.
Keywords Hereditary Angioedema
Angioedema
C1 Inhibitor Deficiency
Coagulation Factor XII Mutations
Management
Guidelines
xmlui.dri2xhtml.METS-1.0.item-coverage Sao Paulo
Language English
Sponsor CSL Boehring
Shire
Date 2018
Published in Clinics. Sao Paulo, v. 73, p. -, 2018.
ISSN 1807-5932 (Sherpa/Romeo, impact factor)
Publisher Hospital Clinicas, Univ Sao Paulo
Extent -
Origin http://dx.doi.org/10.6061/clinics/2018/e310
Access rights Open access Open Access
Type Article
Web of Science ID WOS:000431328700002
SciELO ID S1807-59322018000100303 (statistics in SciELO)
URI https://repositorio.unifesp.br/handle/11600/54325

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