Involvement of the bony orbit in infantile myofibromatosis

Involvement of the bony orbit in infantile myofibromatosis

Author Cruz, AAV Google Scholar
Maia, E. M. Google Scholar
Burmamm, T. G. Google Scholar
Perez, L. C. Google Scholar
Santos, A. N. Google Scholar
Valera, E. T. Google Scholar
Tone, L. G. Google Scholar
Institution Universidade de São Paulo (USP)
Universidade Federal de São Paulo (UNIFESP)
Abstract Infantile myofibromatosis is a rare disorder of infancy that can provoke osteolytic lesions. A 15-day-old infant presented with three round, firm lesions located on the forehead, shoulder, and back. Excisional biopsy of the forehead lesion revealed that the tumor was composed of spindle cells resembling normal smooth muscle arranged in short fascicles. Immunohistochemical staining was positive for vimentin and actin. Five months later, the child presented with three new lesions, including one in the superolateral aspect of the left orbit. It is important to recognize the multicentric form of infantile myofibromatosis because, despite its aggressive clinical presentation, the disease is benign and usually does not require extensive surgery or chemotherapy.
Language English
Date 2004-05-01
Published in Ophthalmic Plastic and Reconstructive Surgery. Philadelphia: Lippincott Williams & Wilkins, v. 20, n. 3, p. 252-254, 2004.
ISSN 0740-9303 (Sherpa/Romeo, impact factor)
Publisher Lippincott Williams & Wilkins
Extent 252-254
Access rights Closed access
Type Article
Web of Science ID WOS:000221622800019

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