Author |
Viégas, Ruy Felipe Melo
![]() ![]() Diniz, Rosiane Viana Zuza ![]() ![]() Viégas, Taciana Mara Rezende Fortes ![]() ![]() Lira Filho, Edgar Bezerra ![]() ![]() Almeida, Dirceu Rodrigues de ![]() ![]() |
Institution | Universidade Federal de São Paulo (UNIFESP) |
Abstract | Total generalized lipodystrophy (Berardinelli--Seip Syndrome) is a rare hereditary disease characterized by insulin-resistant diabetes mellitus and a small quantity of adipose tissue and is of unknown origin. Common cardiovascular alterations related to this syndrome are cardiac hypertrophy and arterial hypertension. This article reports a case of Berardinelli--Seip syndrome and reviews the literature with special emphasis on the cardiovascular manifestations of this syndrome. |
Language | English |
Date | 2000-09-01 |
Published in | Arquivos Brasileiros de Cardiologia. Sociedade Brasileira de Cardiologia - SBC, v. 75, n. 3, p. 246-248, 2000. |
ISSN | 0066-782X (Sherpa/Romeo) |
Publisher | Sociedade Brasileira de Cardiologia - SBC |
Extent | 246-248 |
Origin |
|
Access rights | Open access ![]() |
Type | Article |
SciELO ID | S0066-782X2000000900006 (statistics in SciELO) |
URI | http://repositorio.unifesp.br/handle/11600/1029 |
Name:
S0066-782X2000000900006.pdf
Size: 387.5Kb Format: PDF Description: |
Open file |